Sites of Interest – Supplements
Amino Acid Supplementation
Some nutritionists may supplement your child’s diet with one or more of the offending amino acids: valine, isoleucine, methionine and threonine. It can be difficult to locate a source for the amino acids and may require a compounding pharmacy or hospital pharmacy. The following suppliers are options the amino acids:
L-Carnitine is often prescribed. The following medical articles explain how carnitine binds with propionic acid and leaves the body through the urine:
- L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia. C R Roe, D S Millingoton, D A Maltby, T P Bohan, and C L Hoppel. l
- Propionylcarnitine excretion in propionic and methylmalonic acidurias: a cause of carnitine deficiency.
Di Donato S, Rimoldi M, Garavaglia B, Uziel G.
The following companies distribute L-Carnitine: